Diseases

Achondroplasia

An autosomal dominant disorder that is the most frequent form of short-limb dwarfism. Affected individuals exhibit short stature caused by rhizomelic shortening of the limbs, characteristic facies with frontal bossing and mid-face hypoplasia, exaggerated lumbar lordosis, limitation of elbow extension, GENU VARUM, and trident hand. (Online Mendelian Inheritance in Man, http://www.ncbi.nlm.nih.gov/Omim, MIM#100800, April 20, 2001)

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

An autosomal dominant disorder that is the most frequent form of short-limb dwarfism. Affected individuals exhibit short stature caused by rhizomelic shortening of the limbs, characteristic facies with frontal bossing and mid-face hypoplasia, exaggerated lumbar lordosis, limitation of elbow extension, GENU VARUM, and trident hand. (Online Mendelian Inheritance in Man, http://www.ncbi.nlm.nih.gov/Omim, MIM#100800, April 20, 2001)

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Synonyms

14 entry terms
  • Achondroplasias
  • Achondroplasia, Severe, With Developmental Delay And Acanthosis Nigricans
  • SADDAN
  • SADDAN Dysplasia
  • Severe Achondroplasia with Developmental Delay and Acanthosis Nigricans
  • Skeleton-Skin-Brain Syndrome
  • Dysplasia, SADDAN
  • Dysplasias, SADDAN
  • SADDAN Dysplasias
  • SADDANs
  • Skeleton Skin Brain Syndrome
  • Skeleton-Skin-Brain Syndromes
  • Syndrome, Skeleton-Skin-Brain
  • Syndromes, Skeleton-Skin-Brain

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Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

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NLM Classification

WE 250

AMA Style

References

  1. National Library of Medicine. Achondroplasia. Medical Subject Headings (MeSH). 2026. Unique ID D000130. http://id.nlm.nih.gov/mesh/2026/D000130
  2. Achondroplasia. In: Wikipedia. https://en.wikipedia.org/wiki/Achondroplasia
  3. Achondroplasia. In: Wikidata. https://www.wikidata.org/wiki/Q340594