Diseases

Acute Hemorrhagic Leukoencephalitis

A fulminant and often fatal demyelinating disease of the brain which primarily affects young adults and children. Clinical features include the rapid onset of weakness, SEIZURES, and COMA. It may follow a viral illness or MYCOPLASMA PNEUMONIAE infections but in most instances there is no precipitating event. Pathologic examination reveals marked perivascular demyelination and necrosis of white matter with microhemorrhages. (Adams et al., Principles of Neurology, 6th ed, pp924-5)

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A fulminant and often fatal demyelinating disease of the brain which primarily affects young adults and children. Clinical features include the rapid onset of weakness, SEIZURES, and COMA. It may follow a viral illness or MYCOPLASMA PNEUMONIAE infections but in most instances there is no precipitating event. Pathologic examination reveals marked perivascular demyelination and necrosis of white matter with microhemorrhages. (Adams et al., Principles of Neurology, 6th ed, pp924-5)

MeSH Record

Classification

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MeSH Record

Synonyms

42 entry terms
  • Acute Hemorrhagic Encephalomyelitis
  • Encephalomyelitis, Acute Necrotizing Hemorrhagic
  • Hurst Disease
  • Hurst Syndrome
  • Hurst's Disease
  • Leukoencephalitis Acuta Hemorrhagica
  • Leukoencephalitis, Acute Hemorrhagic
  • Acute Hemorrhagic Encephalomyelitides
  • Acute Hemorrhagic Leukoencephalitides
  • Disease, Hurst
  • Disease, Hurst's
  • Encephalomyelitides, Acute Hemorrhagic
  • Encephalomyelitis, Acute Hemorrhagic
  • Hemorrhagic Encephalomyelitides, Acute
  • Hemorrhagic Encephalomyelitis, Acute
  • Hemorrhagic Leukoencephalitides, Acute
  • Hemorrhagic Leukoencephalitis, Acute
  • Hursts Disease
  • Leukoencephalitides, Acute Hemorrhagic
  • Syndrome, Hurst
  • Encephalitis, Acute Necrotizing
  • Encephalomyelitis, Hemorrhagic Necrotizing
  • Encephalomyelitis, Necrotizing Hemorrhagic
  • Hemorrhagic Encephalomyelitis, Necrotizing
  • Hemorrhagic Necrotizing Encephalomyelitis
  • Leukoencephalitis, Subacute Hemorrhagic
  • Necrotizing Encephalomyelitis, Hemorrhagic
  • Necrotizing Hemorrhagic Encephalomyelitis
  • Acute Necrotizing Encephalitides
  • Acute Necrotizing Encephalitis
  • Encephalitides, Acute Necrotizing
  • Encephalomyelitides, Hemorrhagic Necrotizing
  • Hemorrhagic Encephalomyelitides, Necrotizing
  • Hemorrhagic Leukoencephalitides, Subacute
  • Hemorrhagic Leukoencephalitis, Subacute
  • Leukoencephalitides, Subacute Hemorrhagic
  • Necrotizing Encephalitides, Acute
  • Necrotizing Encephalitis, Acute
  • Necrotizing Encephalomyelitides, Hemorrhagic
  • Necrotizing Hemorrhagic Encephalomyelitides
  • Subacute Hemorrhagic Leukoencephalitides
  • Subacute Hemorrhagic Leukoencephalitis

MeSH Record

Aspects Covered

35 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

1997; was ENCEPHALOMYELITIS, NECROTIZING HEMORRHAGIC 1991-1996 (see under ENCEPHALOMYELITIS 1972-1990); HURST DISEASE was HURST'S DISEASE 1997

MeSH Record

Previous Indexing

  • Demyelinating Diseases (1966-1971)
  • Encephalomyelitis (1966-1971)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Acute Hemorrhagic Leukoencephalitis. Medical Subject Headings (MeSH). 2026. Unique ID D004684. http://id.nlm.nih.gov/mesh/2026/D004684
  2. Acute Hemorrhagic Leukoencephalitis. In: Wikidata. https://www.wikidata.org/wiki/Q18966598