Chemicals and Drugs

Bestrophins

A protein family characterized by a highly conserved N-terminus and four to six transmembrane helices; they function as bicarbonate permeable, calcium-activated chloride channels. Bestrophin-1 (BEST-1) and bestrophin-2 are highly expressed in human RETINAL PIGMENT EPITHELIUM cells and mutations in the BEST-1 gene are associated with VITELLIFORM MACULAR DYSTROPHY, TYPE 2.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A protein family characterized by a highly conserved N-terminus and four to six transmembrane helices; they function as bicarbonate permeable, calcium-activated chloride channels. Bestrophin-1 (BEST-1) and bestrophin-2 are highly expressed in human RETINAL PIGMENT EPITHELIUM cells and mutations in the BEST-1 gene are associated with VITELLIFORM MACULAR DYSTROPHY, TYPE 2.

MeSH Record

Classification

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MeSH Record

Synonyms

11 entry terms
  • Bestrophin
  • Bestrophin Family
  • Bestrophin Proteins
  • BEST-1 Protein
  • BEST-2 Protein
  • Bestrophin-1
  • Bestrophin-2
  • BEST 1 Protein
  • BEST 2 Protein
  • Bestrophin 1
  • Bestrophin 2

MeSH Record

Aspects Covered

30 allowable subheadings

Indexed with the subheadings administration & dosage, adverse effects, agonists, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, deficiency, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.

MeSH Record

History Note

2018

MeSH Record

Previous Indexing

  • Chloride Channels (1999-2017)
  • Eye Proteins (1999-2017)

MeSH Hierarchy

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AMA Style

References

  1. National Library of Medicine. Bestrophins. Medical Subject Headings (MeSH). 2026. Unique ID D000075002. http://id.nlm.nih.gov/mesh/2026/D000075002
  2. Bestrophins. In: Wikidata. https://www.wikidata.org/wiki/Q24720439