Diseases

Caroli Disease

Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.

MeSH Record

Classification

Broader headings

Related Concepts

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MeSH Record

Synonyms

6 entry terms
  • Caroli's Disease
  • Carolis Disease
  • Disease, Caroli
  • Disease, Caroli's
  • Caroli Syndrome
  • Caroli's Syndrome

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2004 (1993)

MeSH Record

Previous Indexing

  • Bile Duct Diseases/congenital (1966-1992)
  • Bile Ducts, Intrahepatic/abnormalities (1985-1992)
  • Biliary Dyskinesia (1966-1984)

MeSH Hierarchy

Tree Numbers

  1. C06w.130.120.127w.500w
  2. C06w.198.184w.500w
  3. C16w.131w.077w.245w.250w
  4. C16w.131w.314.184w.500w
  5. C16w.320w.184w.250w

AMA Style

References

  1. National Library of Medicine. Caroli Disease. Medical Subject Headings (MeSH). 2026. Unique ID D016767. http://id.nlm.nih.gov/mesh/2026/D016767
  2. Caroli Disease. In: Wikipedia. https://en.wikipedia.org/wiki/Caroli_disease
  3. Caroli Disease. In: Wikidata. https://www.wikidata.org/wiki/Q1044327