Chemicals and Drugs

Coproporphyrinogen Oxidase

An enzyme that catalyzes the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX by the conversion of two propionate groups to two vinyl groups. It is the sixth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by CPO gene. Mutations of CPO gene result in HEREDITARY COPROPORPHYRIA.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

An enzyme that catalyzes the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX by the conversion of two propionate groups to two vinyl groups. It is the sixth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by CPO gene. Mutations of CPO gene result in HEREDITARY COPROPORPHYRIA.

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Classification

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Synonyms

5 entry terms
  • Coproporphyrinogen III Oxidases
  • Coproporphyrinogenase
  • III Oxidases, Coproporphyrinogen
  • Oxidase, Coproporphyrinogen
  • Oxidases, Coproporphyrinogen III

MeSH Record

Aspects Covered

28 allowable subheadings

Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.

MeSH Record

History Note

91(76); was see under OXIDOREDUCTASES 1976-90

MeSH Record

Previous Indexing

  • Carboxy-Lyases (1972-1974)
  • Coproporphyrins (1975)
  • Oxidoreductases (1975)
  • Porphyrins (1972-1974)

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AMA Style

References

  1. National Library of Medicine. Coproporphyrinogen Oxidase. Medical Subject Headings (MeSH). 2026. Unique ID D003304. http://id.nlm.nih.gov/mesh/2026/D003304
  2. Coproporphyrinogen Oxidase. In: Wikidata. https://www.wikidata.org/wiki/Q24768974