Diseases

Denys-Drash Syndrome

A disorder of sex development characterized by UROGENITAL ABNORMALITIES; GONADAL DYSGENESIS; and WILMS TUMOR. It is caused by a mutation in the Wilms tumor suppressor gene (GENES, WILMS TUMOR) on chromosome 11.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A disorder of sex development characterized by UROGENITAL ABNORMALITIES; GONADAL DYSGENESIS; and WILMS TUMOR. It is caused by a mutation in the Wilms tumor suppressor gene (GENES, WILMS TUMOR) on chromosome 11.

MeSH Record

Classification

Broader headings

Related Concepts

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MeSH Record

See Also

MeSH Record

Synonyms

7 entry terms
  • Drash Syndrome
  • Nephropathy, Wilms Tumor, and Genital Anomalies
  • Pseudohermaphroditism, Nephron Disorder and Wilms' Tumor
  • Wilms Tumor and Pseudohermaphroditism
  • Denys Drash Syndrome
  • Syndrome, Denys-Drash
  • Syndrome, Drash

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2002

MeSH Record

Previous Indexing

  • Nephroblastoma (1991-2001)
  • Pseudohermaphroditism (1991-2001)

MeSH Hierarchy

Tree Numbers

  1. C04w.557.435w.595w.220w
  2. C04w.588.945w.947.535w.585w.220w
  3. C04w.700w.900w.220w
  4. C12.050.351.875w.253w.096w.562w
  5. C12.050.351.937w.820.535w.585w.220w
  6. C12.050.351.968w.419w.473w.585w.220w
  7. C12.200.706w.316w.096w.562w
  8. C12.200.758w.820.750w.585w.220w
  9. C12.200.777w.419w.473w.585w.220w
  10. C12.800w.316w.096w.562w
  11. C12.900w.820.535w.585w.220w
  12. C12.950w.419w.473w.585w.220w
  13. C12.950w.983.535w.585w.220w
  14. C16w.131w.939w.316w.096w.562w
  15. C16w.320w.700w.900w.220w
  16. C19w.391.119w.096w.562w

AMA Style

References

  1. National Library of Medicine. Denys-Drash Syndrome. Medical Subject Headings (MeSH). 2026. Unique ID D030321. http://id.nlm.nih.gov/mesh/2026/D030321
  2. Denys-Drash Syndrome. In: Wikipedia. https://en.wikipedia.org/wiki/Denys%E2%80%93Drash_syndrome
  3. Denys-Drash Syndrome. In: Wikidata. https://www.wikidata.org/wiki/Q774016