Structured Summary
Abstract
A group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. They are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. They are generally nonprogressive and diffuse. Various forms exist, including anhidrotic and hidrotic dysplasias, FOCAL DERMAL HYPOPLASIA, and aplasia cutis congenita.
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Synonyms
50 entry terms
- Congenital Ectodermal Defect
- Defect, Congenital Ectodermal
- Ectodermal Defect, Congenital
- Congenital Ectodermal Defects
- Defects, Congenital Ectodermal
- Dysplasia, Ectodermal
- Dysplasias, Ectodermal
- Ectodermal Defects, Congenital
- Ectodermal Dysplasias
- Anhidrotic Ectodermal Dysplasia
- Anhydrotic Ectodermal Dysplasia
- Aplasia Cutis Congenita
- Aplasia Cutis Congenita, Nonsyndromic
- Autosomal Dominant Hidrotic Ectodermal Dysplasia
- Clouston Hidrotic Ectodermal Dysplasia
- Clouston Syndrome
- Clouston's Hidrotic Ectodermal Dysplasia
- Clouston's Syndrome
- Ectodermal Dysplasia 2, Hidrotic
- Ectodermal Dysplasia Anhidrotic
- Ectodermal Dysplasia, Anhydrotic
- Ectodermal Dysplasia, Hidrotic
- Ectodermal Dysplasia, Hidrotic, Autosomal Dominant
- Hidrotic Ectodermal Dysplasia
- Hidrotic Ectodermal Dysplasia, Autosomal Dominant
- Hydrotic Ectodermal Dysplasia
- Anhidrotic Ectodermal Dysplasias
- Anhidrotic, Ectodermal Dysplasia
- Anhidrotics, Ectodermal Dysplasia
- Anhydrotic Ectodermal Dysplasias
- Cloustons Syndrome
- Dysplasia Anhidrotic, Ectodermal
- Dysplasia Anhidrotics, Ectodermal
- Dysplasia, Anhidrotic Ectodermal
- Dysplasia, Anhydrotic Ectodermal
- Dysplasia, Hidrotic Ectodermal
- Dysplasia, Hydrotic Ectodermal
- Dysplasias, Anhidrotic Ectodermal
- Dysplasias, Anhydrotic Ectodermal
- Dysplasias, Hidrotic Ectodermal
- Dysplasias, Hydrotic Ectodermal
- Ectodermal Dysplasia, Anhidrotic
- Ectodermal Dysplasia, Hydrotic
- Ectodermal Dysplasias, Anhidrotic
- Ectodermal Dysplasias, Anhydrotic
- Ectodermal Dysplasias, Hydrotic
- Hidrotic Ectodermal Dysplasias
- Hydrotic Ectodermal Dysplasias
- Syndrome, Clouston
- Syndrome, Clouston's
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Aspects Covered
34 allowable subheadings
Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.
MeSH Record
History Note
1965
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WR 218
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References
- National Library of Medicine. Ectodermal Dysplasia. Medical Subject Headings (MeSH). 2026. Unique ID D004476. http://id.nlm.nih.gov/mesh/2026/D004476
- Ectodermal Dysplasia. In: Wikipedia. https://en.wikipedia.org/wiki/Ectodermal_dysplasia
- Ectodermal Dysplasia. In: Wikidata. https://www.wikidata.org/wiki/Q1323713