Structured Summary
Abstract
A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.
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Classification
Broader headings
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MeSH Record
Synonyms
3 entry terms
- Granulomatosis, Lipid
- Erdheim Chester Disease
- Lipid Granulomatosis
MeSH Record
Aspects Covered
35 allowable subheadings
Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.
MeSH Record
History Note
2003
MeSH Record
Previous Indexing
- Histiocytosis (1989-2002)
- Histiocytosis, Langerhans-Cell (1988-2002)
- Histiocytosis, Non-Langerhans-Cell (1991-2002)
- Lipidosis (1979-2002)
- Xanthomatosis (1979-2002)
MeSH Hierarchy
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AMA Style
References
- National Library of Medicine. Erdheim-Chester Disease. Medical Subject Headings (MeSH). 2026. Unique ID D031249. http://id.nlm.nih.gov/mesh/2026/D031249
- Erdheim-Chester Disease. In: Wikipedia. https://en.wikipedia.org/wiki/Erdheim%E2%80%93Chester_disease
- Erdheim-Chester Disease. In: Wikidata. https://www.wikidata.org/wiki/Q1349259