Diseases

Hemolytic Congenital Nonspherocytic Anemia

Any one of a group of congenital hemolytic anemias in which there is no abnormal hemoglobin or spherocytosis and in which there is a defect of glycolysis in the erythrocyte. Common causes include deficiencies in GLUCOSE-6-PHOSPHATE ISOMERASE; PYRUVATE KINASE; and GLUCOSE-6-PHOSPHATE DEHYDROGENASE.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Any one of a group of congenital hemolytic anemias in which there is no abnormal hemoglobin or spherocytosis and in which there is a defect of glycolysis in the erythrocyte. Common causes include deficiencies in GLUCOSE-6-PHOSPHATE ISOMERASE; PYRUVATE KINASE; and GLUCOSE-6-PHOSPHATE DEHYDROGENASE.

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Synonyms

5 entry terms
  • Anemia, Congenital Nonspherocytic Hemolytic
  • Anemia, Hemolytic Congenital, Nonspherocytic
  • Anemia, Hemolytic, Congenital Nonspherocytic
  • Congenital Nonspherocytic Hemolytic Anemia
  • Hemolytic Anemia, Congenital Nonspherocytic

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

91(82)68; was see under ANEMIA, HEMOLYTIC, CONGENITAL 1982-90; was heading 1968-81; was ANEMIA, CONGENITAL NONSPHEROCYTIC HEMOLYTIC 1965-67

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References

  1. National Library of Medicine. Hemolytic Congenital Nonspherocytic Anemia. Medical Subject Headings (MeSH). 2026. Unique ID D000746. http://id.nlm.nih.gov/mesh/2026/D000746
  2. Hemolytic Congenital Nonspherocytic Anemia. In: Wikidata. https://www.wikidata.org/wiki/Q18555220