Diseases

Hemophagocytic Lymphohistiocytosis

A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive.

MeSH Record

Classification

Related Concepts

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MeSH Record

Synonyms

61 entry terms
  • Lymphohistiocytosis, Hemophagocytic
  • Hemophagocytic Lymphohistiocytoses
  • Lymphohistiocytoses, Hemophagocytic
  • Erythrophagocytic Lymphohistiocytosis, Familial
  • Familial Erythrophagocytic Lymphohistiocytosis
  • Familial Hemophagocytic Histiocytosis
  • Familial Hemophagocytic Lymphocytosis
  • Familial Hemophagocytic Lymphohistiocytosis
  • Familial Hemophagocytic Reticulosis
  • Familial Histiocytic Reticulosis
  • Hemophagocytic Lymphohistiocytosis Familial -1
  • Hemophagocytic Lymphohistiocytosis, Familial
  • Hemophagocytic Lymphohistiocytosis, Familial, 1
  • Hemophagocytic Reticulosis, Familial
  • Hemophagocytic Syndrome
  • Hemophagocytic Syndrome, Infection-Associated
  • Hemophagocytic Syndrome, Reactive
  • Hemophagocytic Syndromes
  • Primary Hemophagocytic Hymphohistiocytosis
  • Primary Hemophagocytic Lymphohistiocytosis
  • Reactive Hemophagocytic Syndrome
  • Reticulosis, Familial Histiocytic
  • Erythrophagocytic Lymphohistiocytoses, Familial
  • Familial Erythrophagocytic Lymphohistiocytoses
  • Familial Hemophagocytic Histiocytoses
  • Familial Hemophagocytic Lymphocytoses
  • Familial Hemophagocytic Lymphohistiocytoses
  • Familial Hemophagocytic Reticuloses
  • Familial Histiocytic Reticuloses
  • Hemophagocytic Histiocytoses, Familial
  • Hemophagocytic Histiocytosis, Familial
  • Hemophagocytic Hymphohistiocytoses, Primary
  • Hemophagocytic Hymphohistiocytosis, Primary
  • Hemophagocytic Lymphocytoses, Familial
  • Hemophagocytic Lymphocytosis, Familial
  • Hemophagocytic Lymphohistiocytoses, Familial
  • Hemophagocytic Lymphohistiocytoses, Primary
  • Hemophagocytic Lymphohistiocytosis Familial 1
  • Hemophagocytic Lymphohistiocytosis, Primary
  • Hemophagocytic Reticuloses, Familial
  • Hemophagocytic Syndrome, Infection Associated
  • Histiocytic Reticuloses, Familial
  • Histiocytic Reticulosis, Familial
  • Histiocytoses, Familial Hemophagocytic
  • Histiocytosis, Familial Hemophagocytic
  • Hymphohistiocytoses, Primary Hemophagocytic
  • Hymphohistiocytosis, Primary Hemophagocytic
  • Infection-Associated Hemophagocytic Syndrome
  • Lymphocytoses, Familial Hemophagocytic
  • Lymphocytosis, Familial Hemophagocytic
  • Lymphohistiocytoses, Familial Erythrophagocytic
  • Lymphohistiocytoses, Familial Hemophagocytic
  • Lymphohistiocytoses, Primary Hemophagocytic
  • Lymphohistiocytosis, Familial Erythrophagocytic
  • Lymphohistiocytosis, Familial Hemophagocytic
  • Lymphohistiocytosis, Primary Hemophagocytic
  • Primary Hemophagocytic Hymphohistiocytoses
  • Primary Hemophagocytic Lymphohistiocytoses
  • Reticuloses, Familial Hemophagocytic
  • Reticuloses, Familial Histiocytic
  • Reticulosis, Familial Hemophagocytic

MeSH Record

Aspects Covered

35 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2006; use HISTIOCYTOSIS, NON-LANGERHANS CELL 1990-2005

MeSH Record

Previous Indexing

  • Histiocytosis, Non-Langerhans-Cell (1989-2005)

MeSH Hierarchy

Tree Number

AMA Style

References

  1. National Library of Medicine. Hemophagocytic Lymphohistiocytosis. Medical Subject Headings (MeSH). 2026. Unique ID D051359. http://id.nlm.nih.gov/mesh/2026/D051359
  2. Hemophagocytic Lymphohistiocytosis. In: Wikipedia. https://en.wikipedia.org/wiki/Hemophagocytic_lymphohistiocytosis
  3. Hemophagocytic Lymphohistiocytosis. In: Wikidata. https://www.wikidata.org/wiki/Q1642170