Diseases

Isolated Noncompaction of the Ventricular Myocardium

Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.

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Synonyms

3 entry terms
  • Isolated Non-compaction of the Ventricular Myocardium
  • Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked
  • Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant

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Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2010

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Tree Numbers

  1. C14w.240.400w.660w
  2. C14w.280w.238w.281w.500w
  3. C14w.280w.400w.660w
  4. C16w.131w.077w.477w
  5. C16w.131w.240.400w.655w
  6. C16w.320w.322.370w

AMA Style

References

  1. National Library of Medicine. Isolated Noncompaction of the Ventricular Myocardium. Medical Subject Headings (MeSH). 2026. Unique ID D056830. http://id.nlm.nih.gov/mesh/2026/D056830
  2. Isolated Noncompaction of the Ventricular Myocardium. In: Wikipedia. https://en.wikipedia.org/wiki/Noncompaction_cardiomyopathy
  3. Isolated Noncompaction of the Ventricular Myocardium. In: Wikidata. https://www.wikidata.org/wiki/Q1725245