Structured Summary
Abstract
A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
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Broader headings
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Synonyms
7 entry terms
- Isovaleryl CoA Dehydrogenase
- Isovaleryl-Coenzyme A Dehydrogenase
- CoA Dehydrogenase, Isovaleryl
- Dehydrogenase, Isovaleryl CoA
- Dehydrogenase, Isovaleryl-CoA
- Dehydrogenase, Isovaleryl-Coenzyme A
- Isovaleryl Coenzyme A Dehydrogenase
MeSH Record
Aspects Covered
29 allowable subheadings
Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, deficiency, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.
MeSH Record
History Note
2006(1973)
MeSH Record
Previous Indexing
- Acyl Coenzyme A (1980-1982)
- Coenzyme A (1973-1980)
- Oxidoreductases (1983-2003)
- Oxidoreductases Acting on CH-CH Group Donors (2004-2005)
- Valerates (1973-1982)
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AMA Style
References
- National Library of Medicine. Isovaleryl-CoA Dehydrogenase. Medical Subject Headings (MeSH). 2026. Unique ID D050769. http://id.nlm.nih.gov/mesh/2026/D050769
- Isovaleryl-CoA Dehydrogenase. In: Wikipedia. https://en.wikipedia.org/wiki/Isovaleryl-CoA_dehydrogenase
- Isovaleryl-CoA Dehydrogenase. In: Wikidata. https://www.wikidata.org/wiki/Q87269741