Diseases

Moyamoya Disease

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

MeSH Record

Classification

Related Concepts

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MeSH Record

Synonyms

16 entry terms
  • Cerebrovascular Moyamoya Disease
  • Moya-Moya Disease
  • Moyamoya Syndrome
  • Progressive Intracranial Occlusive Arteropathy (Moyamoya)
  • Disease, Moya-Moya
  • Moya Moya Disease
  • Moyamoya Disease, Classic
  • Moyamoya Disease, Primary
  • Moyamoya Disease, Secondary
  • Classic Moyamoya Disease
  • Disease, Classic Moyamoya
  • Disease, Primary Moyamoya
  • Moyamoya Diseases, Primary
  • Primary Moyamoya Disease
  • Primary Moyamoya Diseases
  • Secondary Moyamoya Disease

MeSH Record

Aspects Covered

35 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

1991(1978)

MeSH Record

Previous Indexing

  • Carotid Artery Diseases (1966-1977)
  • Cerebral Artery Diseases (1966-1977)
  • Cerebrovascular Disorders (1966-1977)

MeSH Hierarchy

Tree Numbers

MeSH Record

NLM Classification

WL 357

AMA Style

References

  1. National Library of Medicine. Moyamoya Disease. Medical Subject Headings (MeSH). 2026. Unique ID D009072. http://id.nlm.nih.gov/mesh/2026/D009072
  2. Moyamoya Disease. In: Wikipedia. https://en.wikipedia.org/wiki/Moyamoya_disease
  3. Moyamoya Disease. In: Wikidata. https://www.wikidata.org/wiki/Q1951267