Diseases

Mucopolysaccharidosis VII

Mucopolysaccharidosis characterized by excessive dermatan and heparan sulfates in the urine and Hurler-like features. It is caused by a deficiency of beta-glucuronidase.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Mucopolysaccharidosis characterized by excessive dermatan and heparan sulfates in the urine and Hurler-like features. It is caused by a deficiency of beta-glucuronidase.

MeSH Record

Classification

Broader headings

Related Concepts

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MeSH Record

Synonyms

20 entry terms
  • GUSB Deficiency
  • Mucopolysaccharidosis 7
  • Mucopolysaccharidosis Type VII
  • Sly Disease
  • Sly Syndrome
  • beta-Glucuronidase Deficiency
  • Deficiencies, GUSB
  • Deficiencies, beta-Glucuronidase
  • Deficiency, GUSB
  • Deficiency, beta-Glucuronidase
  • Disease, Sly
  • GUSB Deficiencies
  • Mucopolysaccharidosis Type VIIs
  • Mucopolysaccharidosis VIIs
  • Syndrome, Sly
  • Type VII, Mucopolysaccharidosis
  • Type VIIs, Mucopolysaccharidosis
  • VIIs, Mucopolysaccharidosis
  • beta Glucuronidase Deficiency
  • beta-Glucuronidase Deficiencies

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

92

MeSH Record

Previous Indexing

  • Mucopolysaccharidoses (1974-1991)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Mucopolysaccharidosis VII. Medical Subject Headings (MeSH). 2026. Unique ID D016538. http://id.nlm.nih.gov/mesh/2026/D016538
  2. Mucopolysaccharidosis VII. In: Wikipedia. https://en.wikipedia.org/wiki/Sly_syndrome
  3. Mucopolysaccharidosis VII. In: Wikidata. https://www.wikidata.org/wiki/Q1750471