Diseases

Neuroacanthocytosis

An inherited autosomal disorder that is characterized by neurodegeneration; orofacial and buccal DYSKINESIAS; CHOREA; and thorny-looking red cells (ACANTHOCYTES). This disorder is due to mutations of chorein which is important in protein trafficking and is encoded by Vps13a on chromosome 9q21.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

An inherited autosomal disorder that is characterized by neurodegeneration; orofacial and buccal DYSKINESIAS; CHOREA; and thorny-looking red cells (ACANTHOCYTES). This disorder is due to mutations of chorein which is important in protein trafficking and is encoded by Vps13a on chromosome 9q21.

MeSH Record

Classification

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MeSH Record

Synonyms

13 entry terms
  • Acanthocytosis with Neurologic Disorder
  • Chorea Acanthocytosis
  • Chorea Acanthocytosis Syndrome
  • Chorea-Acanthocytosis
  • Choreoacanthocytosis
  • Levine-Critchley Syndrome
  • Acanthocytoses, Chorea
  • Acanthocytosis, Chorea
  • Chorea Acanthocytoses
  • Chorea Acanthocytosis Syndromes
  • Chorea-Acanthocytoses
  • Choreoacanthocytoses
  • Levine Critchley Syndrome

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2008 (2000)

MeSH Record

Previous Indexing

  • Acanthocytes (1981-2007)
  • Hematologic Diseases (1982-2007)
  • Movement Disorders (1982-2007)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Neuroacanthocytosis. Medical Subject Headings (MeSH). 2026. Unique ID D054546. http://id.nlm.nih.gov/mesh/2026/D054546
  2. Neuroacanthocytosis. In: Wikipedia. https://en.wikipedia.org/wiki/Neuroacanthocytosis
  3. Neuroacanthocytosis. In: Wikidata. https://www.wikidata.org/wiki/Q746781