Chemicals and Drugs

Ornithine Carbamoyltransferase

A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3.

MeSH Record

Classification

Related Concepts

Knowledge Graph

Loading graph…

Drag nodes to rearrange; hover to trace links; click a node to open its page.

MeSH Record

See Also

MeSH Record

Synonyms

6 entry terms
  • Ornithine Carbamylphosphate Transferase
  • Ornithine Transcarbamylase
  • Carbamoyltransferase, Ornithine
  • Carbamylphosphate Transferase, Ornithine
  • Transcarbamylase, Ornithine
  • Transferase, Ornithine Carbamylphosphate

MeSH Record

Aspects Covered

28 allowable subheadings

Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.

MeSH Record

History Note

1965(1964)

MeSH Hierarchy

Tree Number

AMA Style

References

  1. National Library of Medicine. Ornithine Carbamoyltransferase. Medical Subject Headings (MeSH). 2026. Unique ID D009954. http://id.nlm.nih.gov/mesh/2026/D009954
  2. Ornithine Carbamoyltransferase. In: Wikidata. https://www.wikidata.org/wiki/Q24723588