Chemicals and Drugs

Peroxisome-Targeting Signal 1 Receptor

A cytoplasmic receptor and peroxin that contains a series of TETRATRICOPEPTIDE REPEATS and binds to PEROXISOME TARGETING SIGNAL 1 (SKL-type). It is essential for protein import into PEROXISOMES; mutations in the PEX5 gene are associated with PEROXISOMAL DISORDERS such as ZELLWEGER SYNDROME.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A cytoplasmic receptor and peroxin that contains a series of TETRATRICOPEPTIDE REPEATS and binds to PEROXISOME TARGETING SIGNAL 1 (SKL-type). It is essential for protein import into PEROXISOMES; mutations in the PEX5 gene are associated with PEROXISOMAL DISORDERS such as ZELLWEGER SYNDROME.

MeSH Record

Classification

Broader headings

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MeSH Record

Synonyms

11 entry terms
  • PTS1 Receptor
  • PTS1 Receptors
  • Peroxin PEX5
  • Peroxin-5
  • Peroxisomal Biogenesis Factor 5
  • Peroxisome Receptor 1
  • PEX5, Peroxin
  • Peroxin 5
  • Peroxisome Targeting Signal 1 Receptor
  • Receptor, PTS1
  • Receptors, PTS1

MeSH Record

Aspects Covered

30 allowable subheadings

Indexed with the subheadings administration & dosage, adverse effects, agonists, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, deficiency, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.

MeSH Record

History Note

2018 (1995)

MeSH Hierarchy

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AMA Style

References

  1. National Library of Medicine. Peroxisome-Targeting Signal 1 Receptor. Medical Subject Headings (MeSH). 2026. Unique ID D000074435. http://id.nlm.nih.gov/mesh/2026/D000074435
  2. Peroxisome-Targeting Signal 1 Receptor. In: Wikidata. https://www.wikidata.org/wiki/Q28544028