Structured Summary
Abstract
A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.
MeSH Record
Classification
Broader headings
Related Concepts
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MeSH Record
Synonyms
19 entry terms
- Disseminated Superficial Actinic Porokeratosis
- Keratoderma Palmoplantar, Punctate Type 2
- Porokeratosis Palmaris et Plantaris Disseminata
- Porokeratosis Plantaris Palmaris et Disseminata
- Porokeratosis Plantaris, Palmaris, Et Disseminata
- Porokeratosis of Mibelli
- Porokeratosis, Disseminated Superficial Actinic
- Porokeratosis, Disseminated Superficial Actinic 2
- Porokeratosis, Disseminated Superficial Actinic, 2
- Porokeratosis, Linear
- Porokeratosis, Mibelli
- Porokeratosis, Palmar, Plantar, And Disseminated 1
- Porokeratosis, Palmoplantar
- Porokeratosis, Punctate
- Type 2 Punctate PPK
- Linear Porokeratosis
- Mibelli Porokeratosis
- Palmoplantar Porokeratosis
- Punctate Porokeratosis
MeSH Record
Aspects Covered
34 allowable subheadings
Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.
MeSH Record
Indexing Annotation
do not confuse with PARAKERATOSIS
MeSH Record
History Note
93
MeSH Record
Previous Indexing
- Keratosis (1966-1992)
MeSH Hierarchy
Tree Numbers
AMA Style
References
- National Library of Medicine. Porokeratosis. Medical Subject Headings (MeSH). 2026. Unique ID D017499. http://id.nlm.nih.gov/mesh/2026/D017499
- Porokeratosis. In: Wikipedia. https://en.wikipedia.org/wiki/Porokeratosis
- Porokeratosis. In: Wikidata. https://www.wikidata.org/wiki/Q7230264