Diseases

Primitive Peripheral Neuroectodermal Tumors

A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with EWING SARCOMA.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with EWING SARCOMA.

MeSH Record

Classification

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See Also

MeSH Record

Synonyms

19 entry terms
  • (pPNET) Peripheral Primitive Neuroectodermal Tumors
  • Extracranial Primitive Neuroectodermal Tumor
  • Neuroectodermal Neoplasm, Peripheral Primitive
  • Neuroectodermal Tumor, Peripheral
  • Neuroectodermal Tumor, Peripheral Primitive
  • Neuroectodermal Tumors, Primitive, Peripheral
  • Neuroepithelioma, Peripheral
  • Peripheral Primitive Neuroectodermal Neoplasm
  • Peripheral Primitive Neuroectodermal Tumor
  • Peripheral Primitive Neuroectodermal Tumors
  • Primitive Neuroectodermal Tumor, Extracranial
  • Neuroectodermal Tumors, Peripheral
  • Neuroepitheliomas, Peripheral
  • Peripheral Neuroectodermal Tumor
  • Peripheral Neuroectodermal Tumors
  • Peripheral Neuroepithelioma
  • Peripheral Neuroepitheliomas
  • Tumor, Peripheral Neuroectodermal
  • Tumors, Peripheral Neuroectodermal

MeSH Record

Aspects Covered

39 allowable subheadings

Indexed with the subheadings blood, blood supply, cerebrospinal fluid, chemically induced, chemistry, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, secondary, surgery, therapy, ultrastructure, urine, veterinary, virology.

MeSH Record

Indexing Annotation

coordinate IM with precoordinated organ/neoplasm term (IM)

MeSH Record

History Note

2000(1994)

MeSH Record

Previous Indexing

  • Neoplasms, Germ Cell and Embryonal (1984-1993)
  • Neuroblastoma (1985-1989)
  • Neuroepithelioma (1975-1989)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Primitive Peripheral Neuroectodermal Tumors. Medical Subject Headings (MeSH). 2026. Unique ID D018241. http://id.nlm.nih.gov/mesh/2026/D018241
  2. Primitive Peripheral Neuroectodermal Tumors. In: Wikidata. https://www.wikidata.org/wiki/Q56014124