Structured Summary
Abstract
A subtype of Ehlers-Danlos syndrome (EDS) characterized by vascular pathologies, e.g., AORTIC DISSECTION in addition to common EDS findings, e.g., hyperextensible skin and joints, skin fragility and reduced wound healing capability. It is associated with mutations in collagen type III alpha 1 chain gene (COLLAGEN TYPE III).
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Synonyms
21 entry terms
- EDS IV
- Ehlers Danlos Syndrome Type 4, Autosomal Dominant
- Ehlers Danlos Syndrome, Arterial Type
- Ehlers Danlos Syndrome, Ecchymotic Type
- Ehlers Danlos Syndrome, Sack-Barabas Type
- Ehlers-Danlos Syndrome, Arterial Type
- Ehlers-Danlos Syndrome, Ecchymotic Type
- Ehlers-Danlos Syndrome, Sack-Barabas Type
- Ehlers-Danlos Syndrome, Type IV
- Ehlers-Danlos Syndrome, Type IV, Autosomal Dominant
- Ehlers-Danlos Syndrome, Vascular Type
- Vascular Ehlers-Danlos Syndrome
- Vascular Type Ehlers-Danlos Syndrome
- Ehlers Danlos Syndrome, Sack Barabas Type
- Ehlers-Danlos Syndrome, Vascular
- Ehlers-Danlos Syndromes, Vascular
- Syndrome, Vascular Ehlers-Danlos
- Syndromes, Vascular Ehlers-Danlos
- Type IV Ehlers Danlos Syndrome
- Vascular Ehlers Danlos Syndrome
- Vascular Ehlers-Danlos Syndromes
MeSH Record
Aspects Covered
34 allowable subheadings
Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.
MeSH Record
History Note
2023; see EHLERS-DANLOS SYNDROME 2008-2022
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AMA Style
References
- National Library of Medicine. Type IV Ehlers-Danlos Syndrome. Medical Subject Headings (MeSH). 2026. Unique ID D000094623. http://id.nlm.nih.gov/mesh/2026/D000094623
- Type IV Ehlers-Danlos Syndrome. In: Wikipedia. https://en.wikipedia.org/wiki/Sack%E2%80%93Barabas_syndrome
- Type IV Ehlers-Danlos Syndrome. In: Wikidata. https://www.wikidata.org/wiki/Q3508605