Diseases

Unverricht-Lundborg Syndrome

An autosomal recessive condition characterized by recurrent myoclonic and generalized seizures, ATAXIA, slowly progressive intellectual deterioration, DYSARTHRIA, and intention tremor. Myoclonic seizures are severe and continuous, and tend to be triggered by movement, stress, and sensory stimuli. The age of onset is between 8 and 13 years, and the condition is relatively frequent in the Baltic region, especially Finland. (From Menkes, Textbook of Child Neurology, 5th ed, pp109-110)

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

An autosomal recessive condition characterized by recurrent myoclonic and generalized seizures, ATAXIA, slowly progressive intellectual deterioration, DYSARTHRIA, and intention tremor. Myoclonic seizures are severe and continuous, and tend to be triggered by movement, stress, and sensory stimuli. The age of onset is between 8 and 13 years, and the condition is relatively frequent in the Baltic region, especially Finland. (From Menkes, Textbook of Child Neurology, 5th ed, pp109-110)

MeSH Record

Classification

Broader headings

Related Concepts

Knowledge Graph

Loading graph…

Drag nodes to rearrange; hover to trace links; click a node to open its page.

MeSH Record

See Also

MeSH Record

Synonyms

39 entry terms
  • Baltic Myoclonic Epilepsy
  • Baltic Myoclonus
  • Baltic Myoclonus Epilepsy
  • Epilepsy, Progressive Myoclonic 1
  • Epilepsy, Progressive Myoclonic 1a
  • Epilepsy, Progressive Myoclonic Type 1
  • Epilepsy, Progressive Myoclonus 1
  • Lundborg-Unverricht Syndrome
  • Mediterranean Myoclonic Epilepsy
  • Myoclonic Epilepsy of Unverricht and Lundborg
  • Myoclonus Progressive Epilepsy of Unverricht and Lundborg
  • Progressive Myoclonus Epilepsy 1
  • Progressive Myoclonus Epilepsybaltic Myoclonic Epilepsy
  • Unverricht Disease
  • Unverricht-Lundborg Disease
  • Baltic Myoclonic Epilepsies
  • Baltic Myoclonus Epilepsies
  • Disease, Unverricht
  • Disease, Unverricht-Lundborg
  • Diseases, Unverricht
  • Diseases, Unverricht-Lundborg
  • Epilepsies, Baltic Myoclonic
  • Epilepsies, Baltic Myoclonus
  • Epilepsy, Baltic Myoclonic
  • Epilepsy, Baltic Myoclonus
  • Epilepsy, Mediterranean Myoclonic
  • Lundborg Unverricht Syndrome
  • Myoclonic Epilepsies, Baltic
  • Myoclonic Epilepsy, Baltic
  • Myoclonic Epilepsy, Mediterranean
  • Myoclonus Epilepsies, Baltic
  • Myoclonus Epilepsy, Baltic
  • Myoclonus, Baltic
  • Syndrome, Lundborg-Unverricht
  • Syndrome, Unverricht-Lundborg
  • Unverricht Diseases
  • Unverricht Lundborg Disease
  • Unverricht Lundborg Syndrome
  • Unverricht-Lundborg Diseases

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2000; for LUNDBORG-UNVERRICHT SYNDROME use EPILEPSY, MYOCLONIC 1977-1999

MeSH Record

Previous Indexing

  • Epilepsies, Myoclonic (1977-1999)
  • Epilepsy (1965-1976)
  • Myoclonus (1965-1976)

MeSH Hierarchy

Tree Numbers

  1. C10w.228w.140w.490w.375w.130w.650w.900w
  2. C10w.228w.140w.490w.493w.063w.650w.900w
  3. C10w.574w.500.875w
  4. C16w.320w.400.940w

AMA Style

References

  1. National Library of Medicine. Unverricht-Lundborg Syndrome. Medical Subject Headings (MeSH). 2026. Unique ID D020194. http://id.nlm.nih.gov/mesh/2026/D020194
  2. Unverricht-Lundborg Syndrome. In: Wikipedia. https://en.wikipedia.org/wiki/Unverricht%E2%80%93Lundborg_disease
  3. Unverricht-Lundborg Syndrome. In: Wikidata. https://www.wikidata.org/wiki/Q2356131