Diseases

Donohue Syndrome

Rare autosomal recessive syndrome of extreme insulin resistance due to mutations in the binding domain of INSULIN RECEPTOR. Clinical features include severe intrauterine and postnatal growth restriction, characteristic dysmorphic FACIES; HIRSUTISM; VIRILIZATION; multiple endocrine abnormalities, and early death.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Rare autosomal recessive syndrome of extreme insulin resistance due to mutations in the binding domain of INSULIN RECEPTOR. Clinical features include severe intrauterine and postnatal growth restriction, characteristic dysmorphic FACIES; HIRSUTISM; VIRILIZATION; multiple endocrine abnormalities, and early death.

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Classification

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See Also

MeSH Record

Synonyms

9 entry terms
  • Leprechaunism
  • Leprechaunisms
  • Syndrome, Donohue
  • Mendenhall Syndrome
  • Pineal Hyperplasia, Insulin-Resistant Diabetes Mellitus, And Somatic Abnormalities
  • Rabson-Mendenhall Syndrome
  • Rabson Mendenhall Syndrome
  • Syndrome, Mendenhall
  • Syndrome, Rabson-Mendenhall

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2010

MeSH Record

Previous Indexing

  • Abnormalities, Multiple (2002-2009)
  • Acanthosis Nigricans (2002-2009)
  • Diabetes Mellitus (2000-2009)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Donohue Syndrome. Medical Subject Headings (MeSH). 2026. Unique ID D056731. http://id.nlm.nih.gov/mesh/2026/D056731
  2. Donohue Syndrome. In: Wikipedia. https://en.wikipedia.org/wiki/Donohue_syndrome
  3. Donohue Syndrome. In: Wikidata. https://www.wikidata.org/wiki/Q2467739