Diseases

Hamman-Rich Syndrome

Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.

MeSH Record

Classification

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MeSH Record

Synonyms

11 entry terms
  • Acute Interstitial Pneumonia
  • Acute Interstitial Pneumonitis
  • Hamman-Rich Disease
  • Acute Interstitial Pneumonias
  • Acute Interstitial Pneumonitides
  • Hamman Rich Disease
  • Hamman Rich Syndrome
  • Interstitial Pneumonia, Acute
  • Interstitial Pneumonitis, Acute
  • Pneumonia, Acute Interstitial
  • Pneumonitis, Acute Interstitial

MeSH Record

Aspects Covered

35 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

2020; for HAMMAN-RICH SYNDROME use PULMONARY FIBROSIS 1984-2019; for HAMMAN-RICH SYNDROME use IDIOPATHIC PULMONARY FIBROSIS 2010-2019

MeSH Hierarchy

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AMA Style

References

  1. National Library of Medicine. Hamman-Rich Syndrome. Medical Subject Headings (MeSH). 2026. Unique ID D000080203. http://id.nlm.nih.gov/mesh/2026/D000080203
  2. Hamman-Rich Syndrome. In: Wikipedia. https://en.wikipedia.org/wiki/Acute_interstitial_pneumonitis
  3. Hamman-Rich Syndrome. In: Wikidata. https://www.wikidata.org/wiki/Q424258