Diseases

Idiopathic Pulmonary Fibrosis

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

MeSH Record

Classification

Broader headings

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MeSH Record

Synonyms

22 entry terms
  • Cryptogenic Fibrosing Alveolitis
  • Fibrocystic Pulmonary Dysplasia
  • Fibrosing Alveolitis, Cryptogenic
  • Idiopathic Fibrosing Alveolitis, Chronic Form
  • Pulmonary Fibrosis, Idiopathic
  • Cryptogenic Fibrosing Alveolitides
  • Dysplasia, Fibrocystic Pulmonary
  • Fibrocystic Pulmonary Dysplasias
  • Fibrosing Alveolitides, Cryptogenic
  • Idiopathic Pulmonary Fibroses
  • Pulmonary Dysplasia, Fibrocystic
  • Pulmonary Fibroses, Idiopathic
  • Familial Idiopathic Pulmonary Fibrosis
  • Idiopathic Pulmonary Fibrosis, Familial
  • Interstitial Pneumonitis, Usual
  • Usual Interstitial Pneumonia
  • Interstitial Pneumonia, Usual
  • Pneumonitides, Usual Interstitial
  • Pneumonitis, Usual Interstitial
  • Usual Interstitial Pneumonias
  • Usual Interstitial Pneumonitides
  • Usual Interstitial Pneumonitis

MeSH Record

Aspects Covered

35 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

Indexing Annotation

PULMONARY FIBROSIS is also available

MeSH Record

History Note

2009

MeSH Record

Previous Indexing

  • Pulmonary Fibrosis (1964-2008)

MeSH Hierarchy

Tree Number

  1. C08w.381.483w.652w.500w

AMA Style

References

  1. National Library of Medicine. Idiopathic Pulmonary Fibrosis. Medical Subject Headings (MeSH). 2026. Unique ID D054990. http://id.nlm.nih.gov/mesh/2026/D054990
  2. Idiopathic Pulmonary Fibrosis. In: Wikipedia. https://en.wikipedia.org/wiki/Idiopathic_pulmonary_fibrosis
  3. Idiopathic Pulmonary Fibrosis. In: Wikidata. https://www.wikidata.org/wiki/Q2290446