Diseases

Pseudohypoaldosteronism

A heterogeneous group of disorders characterized by renal electrolyte transport dysfunctions. Congenital forms are rare autosomal disorders characterized by neonatal hypertension, HYPERKALEMIA, increased RENIN activity and ALDOSTERONE concentration. The Type I features HYPERKALEMIA with sodium wasting; Type II, HYPERKALEMIA without sodium wasting. Pseudohypoaldosteronism can be the result of a defective renal electrolyte transport protein or acquired after KIDNEY TRANSPLANTATION.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A heterogeneous group of disorders characterized by renal electrolyte transport dysfunctions. Congenital forms are rare autosomal disorders characterized by neonatal hypertension, HYPERKALEMIA, increased RENIN activity and ALDOSTERONE concentration. The Type I features HYPERKALEMIA with sodium wasting; Type II, HYPERKALEMIA without sodium wasting. Pseudohypoaldosteronism can be the result of a defective renal electrolyte transport protein or acquired after KIDNEY TRANSPLANTATION.

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Synonyms

37 entry terms
  • Pseudohypoaldosteronisms
  • Familial Hyperpotassemia and Hypertension
  • Familial Hypertensive Hyperkalemia
  • Gordon Hyperkalemia-Hypertension Syndrome
  • Hyperpotassemia and Hypertension, Familial
  • Hypertensive Hyperkalemia, Familial
  • Pseudohypoaldosteronism Type 1
  • Pseudohypoaldosteronism Type 1, Autosomal Dominant
  • Pseudohypoaldosteronism Type 1, Autosomal Recessive
  • Pseudohypoaldosteronism Type 2
  • Pseudohypoaldosteronism Type I
  • Pseudohypoaldosteronism Type II
  • Pseudohypoaldosteronism, Type I
  • Pseudohypoaldosteronism, Type I, Autosomal Dominant
  • Pseudohypoaldosteronism, Type I, Autosomal Recessive
  • Pseudohypoaldosteronism, Type II
  • Familial Hypertensive Hyperkalemias
  • Gordon Hyperkalemia Hypertension Syndrome
  • Hyperkalemia, Familial Hypertensive
  • Hyperkalemia-Hypertension Syndrome, Gordon
  • Hyperkalemias, Familial Hypertensive
  • Hypertensive Hyperkalemias, Familial
  • Pseudohypoaldosteronism Type 1s
  • Pseudohypoaldosteronism Type 2s
  • Pseudohypoaldosteronism Type IIs
  • Pseudohypoaldosteronism Type Is
  • Pseudohypoaldosteronisms, Type I
  • Pseudohypoaldosteronisms, Type II
  • Syndrome, Gordon Hyperkalemia-Hypertension
  • Type 1, Pseudohypoaldosteronism
  • Type I Pseudohypoaldosteronism
  • Type I, Pseudohypoaldosteronism
  • Type II Pseudohypoaldosteronism
  • Type II Pseudohypoaldosteronisms
  • Type II, Pseudohypoaldosteronism
  • Type IIs, Pseudohypoaldosteronism
  • Type Is, Pseudohypoaldosteronism

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Aspects Covered

35 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

1991(1988); use RENAL TUBULAR TRANSPORT, INBORN ERRORS 1988-90

MeSH Record

Previous Indexing

  • Aldosterone (1971-1987)
  • Hyperaldosteronism (1975-1980)
  • Renal Tubular Transport, Inborn Errors (1971-1987)

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References

  1. National Library of Medicine. Pseudohypoaldosteronism. Medical Subject Headings (MeSH). 2026. Unique ID D011546. http://id.nlm.nih.gov/mesh/2026/D011546
  2. Pseudohypoaldosteronism. In: Wikipedia. https://en.wikipedia.org/wiki/Pseudohypoaldosteronism
  3. Pseudohypoaldosteronism. In: Wikidata. https://www.wikidata.org/wiki/Q200745