Diseases

Leukocyte-Adhesion Deficiency Syndrome

Rare, autosomal recessive disorder caused by deficiency of the beta 2 integrin receptors (RECEPTORS, LEUKOCYTE-ADHESION) comprising the CD11/CD18 family of glycoproteins. The syndrome is characterized by abnormal adhesion-dependent functions, especially defective tissue emigration of neutrophils, leading to recurrent infection.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Rare, autosomal recessive disorder caused by deficiency of the beta 2 integrin receptors (RECEPTORS, LEUKOCYTE-ADHESION) comprising the CD11/CD18 family of glycoproteins. The syndrome is characterized by abnormal adhesion-dependent functions, especially defective tissue emigration of neutrophils, leading to recurrent infection.

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Classification

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Synonyms

4 entry terms
  • Deficiency Syndrome, Leukocyte-Adhesion
  • Deficiency Syndrome, Leukocyte Adhesion
  • Leukocyte Adhesion Deficiency Syndrome
  • Leukocyte-Adhesion Deficiency Syndromes

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

95

MeSH Record

Previous Indexing

  • Immunologic Deficiency Syndromes (1988-1994)
  • Receptors, Leukocyte-Adhesion/deficiency (1988-1990)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Leukocyte-Adhesion Deficiency Syndrome. Medical Subject Headings (MeSH). 2026. Unique ID D018370. http://id.nlm.nih.gov/mesh/2026/D018370
  2. Leukocyte-Adhesion Deficiency Syndrome. In: Wikipedia. https://en.wikipedia.org/wiki/Leukocyte_adhesion_deficiency
  3. Leukocyte-Adhesion Deficiency Syndrome. In: Wikidata. https://www.wikidata.org/wiki/Q1154422